DH Leung et al. JPGN: 2022 – Volume 74 – Issue 1 – p 96-103. Neurodevelopmental Outcomes in Children With Inherited Liver Disease and Native Liver

In this longitudinal study, the authors evaluated Full Scale Intelligence Quotient (FSIQ) in children with chronic liver disease (mean age 7.6 yrs). Key finding:

• Patients with Alagille syndrome (ALGS) are at increased risk of lower FSIQ (with 29% <85), whereas our data suggest A1AT and PFIC are not

Related blog posts:

• Intellectual Disability in Pediatric Liver Transplantation
• What to Expect After Pediatric Liver Transplantation: Cognitive Function and Quality of Life
• NASPGHAN Alagille Syndrome Webinar