A recent study (M Witt et al. JPGN 2018; 689-94) indicates that among patients with biliary atresia who reached 2 years of life with native liver survival (NLS), they continued to be at risk for progressive liver failure.
- Upon a median follow-up of 16.4 years, NLS rates at 5, 10, 15, 18 years of age were 89%, 72%, 60%, 54%, respectively.
- Corresponding overall survival rates were 98%, 90%, 87%, 87%, respectively
- NLS ended in 37% by liver transplantation (LTx) and in 6% by (pre-transplant) mortality.
- Abstract Link: Prognosis of Biliary Atresia After 2-year Survival With Native Liver
My take: This data provides more precise information for families about prognosis and reinforces the need for careful followup.
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